Peutz - Jegher's syndrome
This syndrome is characterized by pigmentation and gastrointestinal.
Stained smears may occur at birth and usually appear in infants and early childhood, but may occur late. The oral mucosa often becomes permanently infected.
Oral pigmentation is usually dominant and permanent but smears on the lips and skin may disappear after puberty.
Nails are rarely painted in vertical or scattered strips.
Clinical manifestations:
Phenomenon of mucous membranes:
- irregular circular or oval spots pigmented brown and often black, with a diameter of 1 - 5 mm irregularly distributed over the mucous mucosa, gums and lips especially lower. Facial and mucosal pigmentation without clear evidence appears on the intestinal tracts which may exist in relatives.
- Gastrointestinal convulsions may cause frequent episodes of abdominal pain, mucus, vomiting and intestinal dysfunction.
- Rectangular blisters and bleeding.
Skin manifestations:
- The smudges on the face are small, often less than 1 mm and darker and are concentrated around the nose and mouth.
- There may be large smudges on the hands, feet, palms and soles.
Systemic manifestations:
- abdominal pain usually occurs causing intestinal obstruction.
Common rectal haemorrhage and blood vessels may occur with infectious polyps and duodenum.
- Anemia.
Differential diagnosis:
Addison's disease.
- Skin freckles.
Gardner syndrome.
- White spots in the mucous mucosa.
Several factors may cause white spots in the mucous mucosa:
the reasons:
- Infections in the mucous mucosa, such as lesions of the nodules may cause white spots surrounded by an area of acid.
- The saliva leads to oral white spots.
- Marginous mucous spots: painful gray white spots, elevated and surrounded by an acidic area.
- Psoriasis lesions occur most frequently on the lower lip of the inside, tongue and other parts of the mouth, mucous spots are highly contagious and serological tests of the positive vernis.
- Flat lichen
- Pox: mucus.
- Triglyceride: is a white lesion that appears on the tongue with a white false membrane peeled on an acidic base.
- The transplant shows pathogenic pathogens.
- Psoriasis: Hazazia form lesions are associated with several drugs, hepatic diseases and tissue rejection disease.
- White spongy birthmark: Spongy white spongy spots appear on the inner face of the lips, cheeks and sides of the tongue.
- Carcinoma: may exist in the form of white lesion.
- Congenital dysplasia: may cause white spots.
This syndrome is characterized by pigmentation and gastrointestinal.
Stained smears may occur at birth and usually appear in infants and early childhood, but may occur late. The oral mucosa often becomes permanently infected.
Oral pigmentation is usually dominant and permanent but smears on the lips and skin may disappear after puberty.
Nails are rarely painted in vertical or scattered strips.
Clinical manifestations:
Phenomenon of mucous membranes:
- irregular circular or oval spots pigmented brown and often black, with a diameter of 1 - 5 mm irregularly distributed over the mucous mucosa, gums and lips especially lower. Facial and mucosal pigmentation without clear evidence appears on the intestinal tracts which may exist in relatives.
- Gastrointestinal convulsions may cause frequent episodes of abdominal pain, mucus, vomiting and intestinal dysfunction.
- Rectangular blisters and bleeding.
Skin manifestations:
- The smudges on the face are small, often less than 1 mm and darker and are concentrated around the nose and mouth.
- There may be large smudges on the hands, feet, palms and soles.
Systemic manifestations:
- abdominal pain usually occurs causing intestinal obstruction.
Common rectal haemorrhage and blood vessels may occur with infectious polyps and duodenum.
- Anemia.
Differential diagnosis:
Addison's disease.
- Skin freckles.
Gardner syndrome.
- White spots in the mucous mucosa.
Several factors may cause white spots in the mucous mucosa:
the reasons:
- Infections in the mucous mucosa, such as lesions of the nodules may cause white spots surrounded by an area of acid.
- The saliva leads to oral white spots.
- Marginous mucous spots: painful gray white spots, elevated and surrounded by an acidic area.
- Psoriasis lesions occur most frequently on the lower lip of the inside, tongue and other parts of the mouth, mucous spots are highly contagious and serological tests of the positive vernis.
- Flat lichen
- Pox: mucus.
- Triglyceride: is a white lesion that appears on the tongue with a white false membrane peeled on an acidic base.
- The transplant shows pathogenic pathogens.
- Psoriasis: Hazazia form lesions are associated with several drugs, hepatic diseases and tissue rejection disease.
- White spongy birthmark: Spongy white spongy spots appear on the inner face of the lips, cheeks and sides of the tongue.
- Carcinoma: may exist in the form of white lesion.
- Congenital dysplasia: may cause white spots.
Labels
skin diseases