In infantile polycystic disease.. Periportal hepatic fibrosis is associated

In infantile polycystic disease. $$$ AR, Bilateral, there is perinatal, neonatal, infantile and juvenile according to presenting age, the renal severity is inversely proportional to periportal hepatic fibrosis.
A- The kidneys are enlarged and lobulated… (Smooth not lobulated).
B- The kidneys are hypoechoic at ultrasound exam… (Marked hyperechoic).
C- The pattern of inheritance is autosomal dominant… (Autosomal recessive)
D- Periportal hepatic fibrosis is associated… True
E- The prognosis is better when presenting in the neonatal period… (Fatal)
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